典型影像征象 | 线征:骨旁骨肉瘤
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30岁,女性
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右股干骺端外侧皮质有一分叶状肿块,呈致密钙化,边缘光滑,大小约为5.8 x 3.3 x 9.3 cm。无侵袭性骨膜反应。在上方,一薄的透光线将肿瘤与骨皮质分开。
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肿瘤和骨皮质之间呈曲线型透亮线,称为“线征”。
骨旁骨肉瘤(parosteal osteosarcoma)起源于骨皮质附近的成骨性结缔组织,是一种低度恶性肿瘤,预后较好。好发于10~30岁,以长骨干骺端,尤其股骨远端后方最常见,其次为胫骨近端、肱骨近端和股骨近端。骨旁骨肉瘤典型表现为“分叶状的外生性肿块,并伴有靠近骨的中央致密骨化”。肿瘤和邻近皮层之间的透明称为“线征”,在组织学上与位于皮层和肿瘤肿块之间的骨膜相对应。
Case contributed by Dr Matt A. Morgan
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