齿状突加冠综合征
来源: jxradiology
齿状突加冠综合征(crowned dens syndrome)是钙盐晶体在枢椎齿突周围软组织中沉积,影像学征象犹如齿突戴上了一顶皇冠,称为齿状突加冠综合征。齿状突加冠综合征最早由Bouvet等于1985年报告。齿状突加冠综合征的发病率通常被低估。其临床特征主要有突发颈项疼痛,伴随颈部僵硬,偶有发热,红细胞沉降率或超敏C反应蛋白升高,甚至出现颈髓压迫征象。影像学上表现为齿状突上方与周围出现大小不一、高密度的不规则影。CT检查被文献是诊断齿突加冠综合征的金标准。
齿状突加冠综合征可能是一种由羟基磷灰 石结晶和二水焦磷酸钙结晶沉积引起,并有急性颈部疼痛及特征性影像学表现的综合征。容易被误诊为颈椎间盘退变。因此,临床上对有急性颈部疼痛的患者应考虑行枕下区域的影像学检查。
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治疗:
齿状突加冠综合征疼痛可特征性地被非甾体抗炎镇痛药或氢化可的松缓解,两种药物合用效果最好。
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