不同种类的Dandy-Walker畸形
近年来,倾向于把大枕大池(MCM)/Dandy-Walker变异和Dandy-Walker综合症归为同一种胚胎性发育异常的不同类型。当蚓部严重发育不良时,形成完全的Dandy-Walker畸形。仅下部不发育时,形成Dandy-Walker变异。而蚓部轻度发育不良时,形成大枕大池。现在又称为Dandy-Walker谱系疾病,代表广谱的囊性后颅窝畸形。包括Dandy-Walker谱系/复合体,经典Dandy-Walker畸形,小脑蚓部发育不全班扭转,持续存在的Blake囊肿囊肿,巨大小脑延髓池。下图为我个人收集的大枕大池病人:
Case1:
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHBzL2ltYWdlMTA5LjM2MGRvYy5jbi9Eb3dubG9hZEltZy8yMDIxLzAxLzI0MTUvMjEzODgwMDc2XzFfMjAyMTAxMjQwMzQ5NTAzOA==.jpg)
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHBzL2ltYWdlMTA5LjM2MGRvYy5jbi9Eb3dubG9hZEltZy8yMDIxLzAxLzI0MTUvMjEzODgwMDc2XzJfMjAyMTAxMjQwMzQ5NTA1MDc=.jpg)
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHBzL2ltYWdlMTA5LjM2MGRvYy5jbi9Eb3dubG9hZEltZy8yMDIxLzAxLzI0MTUvMjEzODgwMDc2XzNfMjAyMTAxMjQwMzQ5NTE1NA==.jpg)
Case2:
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHBzL2ltYWdlMTA5LjM2MGRvYy5jbi9Eb3dubG9hZEltZy8yMDIxLzAxLzI0MTUvMjEzODgwMDc2XzRfMjAyMTAxMjQwMzQ5NTE2MDE=.jpg)
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHBzL2ltYWdlMTA5LjM2MGRvYy5jbi9Eb3dubG9hZEltZy8yMDIxLzAxLzI0MTUvMjEzODgwMDc2XzVfMjAyMTAxMjQwMzQ5NTIxNjM=.jpg)
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHAvaW1hZ2UxMDkuMzYwZG9jLmNuL0Rvd25sb2FkSW1nLzIwMjEvMDEvMjQxNS8yMTM4ODAwNzZfNl8yMDIxMDEyNDAzNDk1MjY0Nw==.jpg)
Case3:
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHAvaW1hZ2UxMDkuMzYwZG9jLmNuL0Rvd25sb2FkSW1nLzIwMjEvMDEvMjQxNS8yMTM4ODAwNzZfN18yMDIxMDEyNDAzNDk1MzE3OQ==.jpg)
![](http://pic.ikafan.com/imgp/L3Byb3h5L2h0dHAvaW1hZ2UxMDkuMzYwZG9jLmNuL0Rvd25sb2FkSW1nLzIwMjEvMDEvMjQxNS8yMTM4ODAwNzZfOF8yMDIxMDEyNDAzNDk1MzY5NA==.jpg)
![](http://n4.ikafan.com/assetsj/blank.gif)
Case4:
![](http://n4.ikafan.com/assetsj/blank.gif)
![](http://n4.ikafan.com/assetsj/blank.gif)
![](http://n4.ikafan.com/assetsj/blank.gif)
Case5:
![](http://n4.ikafan.com/assetsj/blank.gif)
![](http://n4.ikafan.com/assetsj/blank.gif)
![](http://n4.ikafan.com/assetsj/blank.gif)
工作繁忙,敬请见谅!
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