(左肾门)平滑肌瘤
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病理结果:(左肾门)病变符合平滑肌肿瘤,紧贴肾实质。
肾平滑肌瘤
临床上罕见,占肾脏肿瘤的 0. 18% ,占肾脏良性肿瘤的 2.9% 。肿瘤通常发生于肾脏两极,最常发生于肾包膜,其次是肾盂的平滑肌组织或来源于皮质血管平滑肌。
肾平滑肌瘤并无特征性影像学表现, 肿瘤边界清,CT平扫呈较高密度,增强扫描强化程度低于肾皮质,延迟期倾向于持续均匀强化。
较小的肾平滑肌瘤应与良性肿瘤中的少脂肪血管平滑肌脂肪瘤( AML)、肾癌中的嫌色细胞癌和乳头状癌相鉴别。较大的肾平滑肌瘤还应与大片坏死的乳头状癌、囊性透明细胞癌、 平滑肌肉瘤等相鉴别。
较小的肾平滑肌瘤和少脂肪AML好发性别、 年龄、临床表现均相同,CT和MRI表现也相似。
但平滑肌瘤有完整的包膜,呈圆形、类圆形,起于包膜,位于肾上、下两极及肾外者较多。
而少脂肪AML,多无包膜,呈楔形、类楔形者较多,薄层重建图像并仔细观察其内多可见斑片、 斑点状脂肪密度影,罕有钙化,增强扫描部分肿瘤内可见粗大的血管,多呈快进快出强化模式。
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